Ferreira Sheila Maria Ag, Ferreira Alberto G, Meguins Lucas Crociati, Neto Dionísio B Carvalho
Fundação Luiz Décourt, Cardiology Department, Rua Jerônimo Pimentel, Umarizal, Brazil.
J Cardiovasc Med (Hagerstown). 2009 Oct;10(10):795-7. doi: 10.2459/JCM.0b013e32832ce9b1.
Cor triatriatum sinister (CTS) is an extremely rare congenital cardiac malformation characterized by the presence of a fibromuscular membrane subdividing the left atrium into two chambers. Although respiratory symptoms are often observed in patients with this anomaly, wheezing is an unusual clinical presentation. We report on a child, born and resident in the Brazilian Amazonia, with a history of recurrent episodes of 'asthma' who was subsequently found to have CTS. After successful surgical correction of the cardiac congenital malformation, the child became symptom free. This case highlights the importance of investigating by cardiologic assessment children with worsening wheezing that do not respond well to appropriate medical management.
左房三房心(CTS)是一种极其罕见的先天性心脏畸形,其特征是存在将左心房分为两个腔室的纤维肌性隔膜。虽然患有这种畸形的患者常出现呼吸道症状,但喘息是一种不常见的临床表现。我们报告了一名出生并居住在巴西亚马逊地区的儿童,有反复发作的“哮喘”病史,随后被发现患有CTS。在成功手术矫正心脏先天性畸形后,该儿童症状消失。这个病例强调了对喘息加重且对适当药物治疗反应不佳的儿童进行心脏评估的重要性。