Département de Médecine Physique et Réadaptation, Centre Hospitalo-Universitaire de Montpellier Nîmes, CHU Carémeau, Place du Pr Robert Debré, 30029 Nîmes Cedex 09, France.
Eur Spine J. 2010 Jul;19 Suppl 2(Suppl 2):S87-90. doi: 10.1007/s00586-009-1086-6. Epub 2009 Jul 10.
Camptocormia is an abnormal posture with marked flexion of thoracolumbar spine that abates in the recumbent position. Camptocormia has been described in various neurological (Parkinsonism), muscular (myopathy), psychogenic or orthopedic disorders. There are several hypotheses that can explain this impaired posture but they are usually related to the concomitant pathologies. We report the first case of a patient with confirmed myotonic dystrophy addressed to our medical center for impaired posture who underwent extensive medical exams and explorations because of a myotonic hand. Axial weakness and muscle atrophy, validated by CT-scan imaging, are discussed independent of the concomitant pathology (Parkinson, myopathy).
脊柱前屈畸形是一种异常姿势，表现为胸腰椎显著弯曲，在卧位时缓解。脊柱前屈畸形可见于各种神经源性（帕金森病）、肌源性（肌病）、心因性或骨科疾病。有几种假说可以解释这种姿势障碍，但通常与并存的病理有关。我们报告首例以姿势障碍就诊于我院的明确诊断为肌强直性营养不良的患者，其因肌强直性手接受了广泛的医学检查和探索。我们讨论了轴性无力和肌肉萎缩，这些通过 CT 扫描成像得到证实，且与并存的病理（帕金森病、肌病）无关。
