Densupsoontorn N, Jirapinyo P, Aanpreung P, Laohapensang M, Parichatikanond P
Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.
Acta Paediatr. 2009 Nov;98(11):1847-9. doi: 10.1111/j.1651-2227.2009.01432.x. Epub 2009 Jul 22.
A 6-month-old male infant who presented with abdominal distension and congenital chylous ascites was diagnosed. He was initially refractory to conservative therapy, and then was completely cured with ligation of megalymphatics and fibrin glue application. Immunoperoxidase staining for CD31 on the biopsied peritoneal tissues highlighted the lining cells of lymphatic spaces, which indicated lymphangiectasia.
This case emphasizes the effectiveness of lymphatic ligation of the retroperitoneal megalymphatics in conjunction with fibrin glue application to cure congenital lymphangiectasia.
一名6个月大的男婴因腹胀和先天性乳糜性腹水就诊，被诊断为此病。他最初对保守治疗无效，随后通过结扎巨大淋巴管并应用纤维蛋白胶而完全治愈。对活检的腹膜组织进行CD31免疫过氧化物酶染色突出显示了淋巴间隙的衬里细胞，这表明存在淋巴管扩张。
该病例强调了腹膜后巨大淋巴管结扎联合应用纤维蛋白胶治疗先天性淋巴管扩张的有效性。
