Mayo Work Study Program, Mayo Clinic, Rochester, MN 55905, USA.
J Cardiol. 2009 Aug;54(1):162-6. doi: 10.1016/j.jjcc.2008.11.002. Epub 2009 Jan 4.
Although primary cardiac amyloidosis is a rare affliction of the heart, its clinical and pathology features have been well described. Patients generally present with exertional dyspnea, chest discomfort, or congestive heart failure. Cardiac imaging typically reveals ventricular wall thickening, systolic and diastolic dysfunction, valvular thickening, and pericardial effusion. In the case reported herein, a patient with suspected cardiac amyloid demonstrated electrocardiographic and echocardiographic findings that were not only inconsistent with typical depositional patterns, but also potentially suggestive of endomyocardial disease.
虽然原发性心脏淀粉样变是一种罕见的心脏疾病,但它的临床和病理特征已经得到了很好的描述。患者通常表现为运动性呼吸困难、胸痛或充血性心力衰竭。心脏影像学检查通常显示心室壁增厚、收缩和舒张功能障碍、瓣膜增厚和心包积液。在本文报告的病例中,一名疑似心脏淀粉样变的患者表现出的心电图和超声心动图结果不仅与典型的沉积模式不一致,而且还可能提示为心肌疾病。