Morris Luc G T, Rihani Jordan, Lebowitz Richard A, Wang Beverly Y
Department of Otolaryngology, New York University School of Medicine, 550 First Avenue, HCC-3C, New York, NY 10016, USA.
Head Neck Pathol. 2009 Jun;3(2):169-73. doi: 10.1007/s12105-009-0121-6. Epub 2009 Jun 10.
Chondromyxoid fibroma (CMF) is a rare benign primary tumor which usually affects the metaphyses of the long bone of the lower extremities in childhood and young adults. Rarely, CMF occurs in the skull base and parasinuses, which may be difficult to distinguish from chondrosarcoma or chordoma and other tumors in the head. It is composed of chondroid, myxoid, and fibrous tissue growth in a lobular pattern, infrequently with calcifications. We report one case of CMF involving the sphenoid sinus mimicking a chondrosarcoma. The tumor mass showed calcifications on images and histology.
软骨黏液样纤维瘤(CMF)是一种罕见的原发性良性肿瘤,通常在儿童和青年时期累及下肢长骨的干骺端。CMF极少发生于颅底和鼻窦,可能难以与软骨肉瘤、脊索瘤及头部的其他肿瘤相鉴别。它由呈小叶状生长的软骨样、黏液样和纤维组织构成,很少有钙化。我们报告1例累及蝶窦、酷似软骨肉瘤的CMF病例。该肿瘤块在影像学和组织学上均显示有钙化。