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上肢完全性裂缺:一种非常罕见的畸形。

Complete cleft of the upper limb: A very rare anomaly.

作者信息

Bhatt Yogesh C, Bakshi Harpreet S, Vyas Kinnari A, Ambat Girish S, Laad Hitesh, Panse Nikhil S

机构信息

Department of Plastic Surgery, SSG Hospital and Medical College, Vadodara, Gujarat-390 001, India.

出版信息

Indian J Plast Surg. 2008 Jul;41(2):195-9. doi: 10.4103/0970-0358.44842.

DOI:10.4103/0970-0358.44842
PMID:19753263
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2740503/
Abstract

BACKGROUND

We describe here a very rare congenital deformity that involves the splitting of the right upper limb with the superior limb articulating with the shoulder joint, and the inferior limb laterally attached to the chest wall.

MATERIAL AND METHODS

The child with this rare split limb was treated by transferring the inferior limb on an islanded pedicle to the superior one while creating the hand.

RESULTS

A unified limb was reconstructed while creating the hand without any compromise on the existing function and vascularity. The patient is on regular follow-up and further staged procedures have been planned to provide a better functional and aesthetic limb.

CONCLUSION

The congenital deformity described here has not been mentioned in world literature so far and its embryological basis is a matter of discussion. Opinions regarding further management of this anomaly are invited from experts in the field.

摘要

背景

我们在此描述一种极为罕见的先天性畸形,即右上肢分裂,上肢近端与肩关节相连,下肢则横向附着于胸壁。

材料与方法

对患有这种罕见肢体分裂的患儿进行治疗,在制作手部的同时,将带蒂岛状的下肢转移至上肢近端。

结果

在制作手部的同时重建了一个完整的肢体,且未对现有功能和血管造成任何损害。患者正在接受定期随访,并且已计划进行进一步的分期手术,以提供功能和美观更佳的肢体。

结论

目前世界文献中尚未提及此处所描述的先天性畸形,其胚胎学基础仍有待探讨。我们邀请该领域的专家就这种异常情况的进一步治疗发表意见。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6648/2740503/84f525600588/IJPS-41-195-g016.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6648/2740503/ed64e4758277/IJPS-41-195-g001.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6648/2740503/b87357c941e4/IJPS-41-195-g003.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6648/2740503/84f525600588/IJPS-41-195-g016.jpg

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本文引用的文献

1
Ulnar dimelia.尺侧重复畸形
J Bone Joint Surg Br. 1960 Aug;42-B:549-55. doi: 10.1302/0301-620X.42B3.549.
2
Morphological patterns in limb deficiencies and duplications.肢体缺损与重复的形态学模式。
Am J Anat. 1951 Sep;89(2):135-93. doi: 10.1002/aja.1000890202.
3
Mirror hand anomaly; a case presentation.镜像手畸形;病例报告。
Plast Reconstr Surg Transplant Bull. 1958 Jan;21(1):80-3. doi: 10.1097/00006534-195801000-00008.
4
Symbrachydactyly instead of atypical cleft hand.短指并指畸形而非典型裂手畸形。
Plast Reconstr Surg. 1993 Jan;91(1):196. doi: 10.1097/00006534-199301000-00045.
5
Mirror hand treated by true pollicization.
J Hand Surg Br. 1986 Oct;11(3):320-36. doi: 10.1016/0266-7681(86)90152-x.
6
Soft-tissue anatomy of mirror hand.
J Hand Surg Br. 1986 Oct;11(3):307-19. doi: 10.1016/0266-7681(86)90151-8.
7
Cleft hand without absence of a finger.
Handchir Mikrochir Plast Chir. 1988 Jul;20(4):184-8.
8
Teratogenic relationship between polydactyly, syndactyly and cleft hand.
J Hand Surg Br. 1990 May;15(2):201-9. doi: 10.1016/0266-7681_90_90125-n.