Liu Ruolan, Hao Junwei, Dayao Carlos S, Shi Fu-Dong, Campagnolo Denise I
Department of Neurology, Barrow Neurological Institute, St. Joseph's Hospital and Medical Center, 350 W Thomas Road, Phoenix, AZ 85013-4496, USA.
Exp Neurol. 2009 Dec;220(2):366-73. doi: 10.1016/j.expneurol.2009.09.022. Epub 2009 Oct 7.
T-bet, a tissue-specific transcription factor, controls T helper 1 (Th1) cell differentiation and IFN-production. Given the reciprocal relationship between Th1 and other types of helper T cells, we hypothesized that T-bet impacts multiple helper and regulatory T (Treg) cells, thereby influencing the magnitude of autoimmune disease. We tested this hypothesis in an experimental model of autoimmune myasthenia gravis (EAMG) of mice. Myasthenia gravis (MG) and EAMG are T cell-driven, IgG autoantibody-mediated disorders that destroy muscles by attacking the target antigen acetylcholine receptor (AChR) or other antigens of skeletal muscle at neuromuscular junctions. We show that, compared to wild-type mice, AChR-primed T-bet(-/-) mice are less susceptible to EAMG. This phenotype is associated with a reduction of autoreactive Th1 cells and augmentation of Th2 and Th17 cells as well as an upregulation of Foxp3 expression by T-bet(-/-)CD4(+)CD25(+) Treg cells. Thus, in our model, T-bet not only specifies the Th1 lineage but also has a broad influence on autoreactive Th2, Th17 and Treg cells. These coordinated effects reduce the genesis of pathogenic antibodies and protect against B cell-mediated EAMG.
T-bet是一种组织特异性转录因子,可控制辅助性T细胞1(Th1)的分化和干扰素的产生。鉴于Th1与其他类型辅助性T细胞之间的相互关系,我们推测T-bet会影响多种辅助性T细胞和调节性T(Treg)细胞,从而影响自身免疫性疾病的严重程度。我们在小鼠自身免疫性重症肌无力(EAMG)的实验模型中验证了这一假设。重症肌无力(MG)和EAMG是由T细胞驱动、IgG自身抗体介导的疾病,通过攻击神经肌肉接头处的靶抗原乙酰胆碱受体(AChR)或骨骼肌的其他抗原破坏肌肉。我们发现,与野生型小鼠相比,用AChR致敏的T-bet基因敲除(-/-)小鼠对EAMG的易感性较低。这种表型与自身反应性Th1细胞减少、Th₂ 和Th17细胞增加以及T-bet(-/-)CD4(+)CD25(+)Treg细胞中Foxp3表达上调有关。因此,在我们的模型中,T-bet不仅决定了Th1谱系,而且对自身反应性Th2、Th17和Treg细胞有广泛影响。这些协同效应减少了致病性抗体的产生,并预防了B细胞介导的EAMG。