Suryanarayanan R, Lesser T H
Department of Otolaryngology, Aintree University Hospitals National Health Service Foundation Trust, Liverpool, UK.
J Laryngol Otol. 2010 May;124(5):560-3. doi: 10.1017/S0022215109991411. Epub 2009 Oct 26.
To report the coexistence of multiple tegmen defects, forming a 'honeycomb' pattern, together with dehiscence of the superior semicircular canal.
We describe three cases in which the above findings were noted, and we review the relevant literature.
Superior semicircular canal dehiscence is defined as the absence of portions of bone over the canal along the floor of the middle fossa. Most published articles describe the defect as an isolated finding which is either unilateral or bilateral. Studies on temporal bones show either a defect over the superior semicircular canal or isolated defects over the tegmen. We describe three cases in which we found multiple tegmen defects, giving a characteristic honeycomb appearance, coexisting with dehiscence over the superior semicircular canal. This finding, which supports the theory of a developmental defect as the origin of the condition, has not previously been reported. A literature review is presented, with discussion of the aetiology and management of superior semicircular canal dehiscence.
报告多个骨盖缺损并存形成“蜂窝”样图案以及上半规管裂开的情况。
我们描述了3例观察到上述表现的病例，并对相关文献进行了综述。
上半规管裂开定义为中颅窝底部沿半规管的部分骨质缺失。大多数已发表的文章将该缺损描述为孤立性发现，可为单侧或双侧。颞骨研究显示上半规管存在缺损或骨盖存在孤立性缺损。我们描述了3例发现多个骨盖缺损并呈现特征性蜂窝样外观且与上半规管裂开并存的病例。这一发现支持了该病起源于发育缺陷的理论，此前尚未见报道。本文进行了文献综述，并讨论了上半规管裂开的病因及治疗。
