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一名患有新发抗MuSK介导的重症肌无力的母亲所生婴儿的短暂性新生儿重症肌无力。

Transient neonatal myasthenia gravis in a baby born to a mother with new-onset anti-MuSK-mediated myasthenia gravis.

作者信息

O'carroll Peter, Bertorini Tulio E, Jacob Glady, Mitchell Christopher W, Graff Justin

机构信息

University of Tennessee Health Science Center, Memphis, TN, USA.

出版信息

J Clin Neuromuscul Dis. 2009 Dec;11(2):69-71. doi: 10.1097/CND.0b013e3181a78280.

DOI:10.1097/CND.0b013e3181a78280
PMID:19955986
Abstract

We describe a 30-year-old pregnant woman with undiagnosed weakness who delivered a severely weak neonate. Subsequent workup of the mother revealed myasthenia gravis with muscle-specific kinase antibodies. The infant responded to intravenous immunoglobulin and symptoms normalized. He was presumed to have an anti-muscle-specific kinase-mediated transient neonatal myasthenia gravis.

摘要

我们描述了一名30岁未被诊断出肌无力的孕妇,她产下了一名极度虚弱的新生儿。随后对母亲的检查发现其患有伴有肌肉特异性激酶抗体的重症肌无力。婴儿对静脉注射免疫球蛋白有反应,症状恢复正常。推测他患有抗肌肉特异性激酶介导的短暂性新生儿重症肌无力。

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Transient neonatal myasthenia gravis in a baby born to a mother with new-onset anti-MuSK-mediated myasthenia gravis.一名患有新发抗MuSK介导的重症肌无力的母亲所生婴儿的短暂性新生儿重症肌无力。
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