Kaplan S B, Kemp S S, Oh K S
Department of Radiology, Presbyterian-University Hospital, Pittsburgh, Pennsylvania.
Radiol Clin North Am. 1991 Mar;29(2):195-218.
Congenital anomalies of the pediatric skull are caused by a diverse group of disorders. For the purposes of this discussion, these entities can be classified according to the radiographic appearance of the skull, which may be similar in a variety of different diseases. Enlarged parietal foramina, sinus pericranii, aplasia cutis congenita, anterior fontanelle dermoid, cephaloceles, and craniolacunia are all examples of loceles, and craniolacunia are all examples of calvarial defects. Although there are numerous causes for wormian bones (Table 1), OI, cleidocranial dysplasia, congenital hypothyroidism, and hypophosphatasia are disorders that are commonly associated with defective ossification and the appearance of wormian bones. Osteopetrosis is an important example of rare bony dysplasias that cause sclerosis and hyperostosis of the skull. A partial list of other disorders causing similar radiographic findings is found in Table 2. Craniosynostosis results in an abnormality of skull shape. The suture(s) involved may be predicted by the deformed calvarial configuration. Knowledge of the growth and development of the skull and an understanding of the varied causes of congenital skull anomalies can enable the radiologist to provide the diagnosis or an informed differential diagnosis when confronted with a specific radiographic finding.
小儿颅骨先天性异常由多种疾病引起。为便于讨论,这些病症可根据颅骨的影像学表现进行分类,在多种不同疾病中其表现可能相似。顶骨孔扩大、头皮下静脉丛瘤、先天性皮肤发育不全、前囟皮样囊肿、脑膨出和颅骨缺损均为例,颅骨缺损都是颅盖骨缺损的例子。虽然缝间骨有多种成因(表1),但成骨不全、锁骨颅骨发育不全、先天性甲状腺功能减退和低磷酸酯酶症是通常与骨化缺陷及缝间骨出现相关的病症。骨质石化症是导致颅骨硬化和骨质增生的罕见骨发育异常的一个重要例子。表2列出了导致类似影像学表现的其他部分病症。颅缝早闭会导致颅骨形状异常。受累的缝线可通过变形的颅盖骨形态来预测。了解颅骨的生长发育以及先天性颅骨异常的各种成因,可使放射科医生在面对特定影像学表现时能够做出诊断或提供有依据的鉴别诊断。