Department of Lymphology, Hôpital Cognacq-Jay, 15, rue Eugène Millon, 75015 Paris, France.
J Plast Reconstr Aesthet Surg. 2010 Nov;63(11):1883-5. doi: 10.1016/j.bjps.2009.11.019. Epub 2009 Dec 9.
Lymphangioma circumscriptum, a rare, benign disease that can be either congenital or acquired, involves the deep dermis and subcutaneous lymphatics.
This study aims to analyse the efficacy of surgical resection of vulva lymphangioma circumscriptum (VLC).
Between January 2000 and December 2008, eight consecutive women referred to our centre and treated surgically for VLC were included in the study. VLC was responsible for recurrent lymph oozing in seven cases. All women were treated by the same plastic surgeon specialising in lymphatic diseases.
The first surgery was performed after a median interval of 5.4 years since VLC onset. The first cutaneous resection included the labia majora of all women and labia minora of five and clitoral hood of four. Five women experienced rapidly recurrent vesicles associated with lymph oozing and underwent resection again (once: two women, twice: three women). The second resection was performed 4-6 months after the first, whereas the third took place 1-6 years after the second. Five women had moderate and transitory post-surgical lymph oozing. After a median follow-up of 53 months after the last surgery, seven of the eight women were free from symptom.
Surgical resection is an effective and well-tolerated therapy for VLC in most women. Lesion recurrence is frequent but resection can be repeated several times with no adverse effects.
淋巴管瘤是一种罕见的良性疾病，可分为先天性和获得性，涉及真皮深部和皮下淋巴管。
本研究旨在分析外阴淋巴管瘤切除术（VLC）的疗效。
2000 年 1 月至 2008 年 12 月，连续 8 例因 VLC 就诊并接受手术治疗的女性患者纳入本研究。7 例因反复发作淋巴液渗出而就诊。所有患者均由同一位擅长淋巴疾病的整形医生治疗。
第一次手术距 VLC 发病的平均间隔时间为 5.4 年。初次皮肤切除包括所有女性的大阴唇、5 例小阴唇和 4 例阴蒂包皮。5 例患者迅速出现复发性水疱伴淋巴液渗出，并再次接受切除术（2 例 1 次，3 例 2 次）。第二次切除在第一次切除后 4-6 个月进行，第三次切除在第二次切除后 1-6 年进行。5 例患者有中度且短暂的术后淋巴液渗出。末次手术后平均随访 53 个月，8 例患者中 7 例症状缓解。
手术切除是大多数女性 VLC 的有效且耐受良好的治疗方法。病变复发较为常见，但可多次切除而无不良影响。
