Division of Hematology and Oncology, Department of Internal Medicine, University of Michigan, Ann Arbor, MI, USA.
Hematology Am Soc Hematol Educ Program. 2009:461-76. doi: 10.1182/asheducation-2009.1.461.
Given its relative rarity, it may at first seem surprising that chronic myeloid leukemia (CML) has garnered so much attention over the last decade. Yet, the advances in molecular pathogenesis that have been derived from studying this leukemia have clearly benefited all of oncology. Moreover, the strides in drug design and development that have also ensued around CML have given rise to what others have called a molecular revolution in cancer therapy. While a majority of patients with chronic phase CML (CP-CML) have an excellent durable response to imatinib (Gleevec, Novartis, Basel, Switzerland), a clear minority will unfortunately have signs of primary or secondary resistance to therapy. Significant efforts geared toward understanding the molecular mechanisms of imatinib resistance have yielded valuable insights into the biology of drug trafficking into and out of cells, epigenetic control of cellular processes, alterations in enzymatic structures, and the rational structural-based design of small molecule enzyme inhibitors. This review will describe the efforts at understanding the pathogenesis of imatinib resistance and the molecular rationale for the development of second- and now third-generation therapies for patients with CML.
鉴于其相对罕见,慢性髓性白血病(CML)在过去十年中受到如此多的关注,这可能起初令人惊讶。然而,从研究这种白血病中得出的分子发病机制的进展显然使所有肿瘤学都受益。此外,围绕 CML 进行的药物设计和开发方面的进展也带来了其他人所称的癌症治疗中的分子革命。虽然大多数慢性期 CML(CP-CML)患者对伊马替尼(格列卫,诺华,巴塞尔,瑞士)有极好的持久反应,但不幸的是,少数患者会出现对治疗的原发性或继发性耐药迹象。为了解伊马替尼耐药的分子机制而进行的大量努力为了解药物进出细胞的转运、细胞过程的表观遗传控制、酶结构的改变以及小分子酶抑制剂的合理基于结构的设计的生物学提供了有价值的见解。这篇综述将描述了解伊马替尼耐药发病机制的努力,以及为 CML 患者开发第二代和现在第三代治疗方法的分子原理。