Martínez-Lage J F, Acosta J, Sola J, Poza M
Regional Service of Neurosurgery, Hospital Universitario Virgen de la Arrixaca, Murcia, Spain.
Childs Nerv Syst. 1996 Jul;12(7):409-12. doi: 10.1007/BF00395097.
Desmoid tumors are uncommon benign neoplasms of fibroblastic origin, frequently presenting in the abdomen or abdominal wall of adults. This tumor is well known to general surgeons and pathologists, but it has rarely been reported in the neurosurgical literature. We describe a neonate who presented with a right temporal subscalp tumor at birth. In spite of initial apparent total removal, the tumor recurred twice. We discuss the diagnostic pitfalls encountered in assessing this tumor and the difficulties in distinguishing, in the excised specimens, between desmoid and reactive fibrosis. We suggest that desmoid tumor should be considered in the differential diagnosis of scalp and calvarial masses in children. Complete excision is required to prevent recurrences, and sometimes a multidisciplinary team is needed to secure margin-free resection.
硬纤维瘤是一种罕见的起源于成纤维细胞的良性肿瘤，常见于成年人的腹部或腹壁。这种肿瘤为普通外科医生和病理学家所熟知，但在神经外科文献中鲜有报道。我们描述了一名出生时即出现右侧颞部头皮下肿瘤的新生儿。尽管最初看似完全切除，但肿瘤复发了两次。我们讨论了评估该肿瘤时遇到的诊断陷阱，以及在切除标本中区分硬纤维瘤和反应性纤维化的困难。我们建议在儿童头皮和颅骨肿物的鉴别诊断中应考虑硬纤维瘤。需要完整切除以防止复发，有时需要多学科团队来确保无瘤切缘切除。
