Department of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, Italy.
Cardiol Res Pract. 2009;2009:976190. doi: 10.4061/2009/976190. Epub 2009 Nov 4.
We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta.
我们呈现了一例 54 岁女性病例，其弥漫性先天性主动脉瓣上狭窄（SVAS）伴严重主动脉瓣关闭不全和主动脉瓣环重度钙化。手术修复包括切除升主动脉、补片扩大发育不良的主动脉根部和瓣环、植入 20 毫米涤纶管状移植物（Vascutek，Renfrewshire，英国）和机械瓣置换主动脉瓣（Sorin，都灵，意大利）。术后超声心动图显示人工瓣膜功能正常，术后三维 CT 扫描显示重建升主动脉形态正常。
