Ata Yusuf, Turk Tamer, Demir Mihriban, Ata Filiz, Yavuz Senol
Department of Cardiovascular Surgery, Bursa Yuksek Ihtisas Education and Research Hospital, 16330 Bursa, Turkey.
Case Rep Med. 2009;2009:536424. doi: 10.1155/2009/536424. Epub 2009 Dec 20.
Behcet's disease (BD) is a chronic, recurrent, systemic disease that is characterized by oral and genital ulcers and oculocutaneous inflammatory lesions. Cardiovascular involvement especially large artery involvement is a serious and vital complication of BD. Pseudoaneurysms in the major arteries may be the cause of sudden death in BD. In our case a pulsatile abdominal mass was determined to be an aortic pseudoaneurysm associated with BD and an aortocaval fistula. Here we report this case and a short review of literature because this is the first reported aortocaval fistula in a BD patient in English literature.
白塞病(BD)是一种慢性、复发性全身性疾病,其特征为口腔和生殖器溃疡以及眼皮肤炎性病变。心血管受累尤其是大动脉受累是白塞病的一种严重且关键的并发症。主要动脉的假性动脉瘤可能是白塞病患者猝死的原因。在我们的病例中,一个搏动性腹部肿块被确定为与白塞病相关的主动脉假性动脉瘤以及主动脉腔静脉瘘。在此我们报告该病例并对文献进行简要综述,因为这是英文文献中首次报道的白塞病患者发生主动脉腔静脉瘘的病例。