Ullery Brant W, Pochettino Alberto, Wang Grace J, Jackson Benjamin M, Fairman Ronald M, Woo Edward Y
Department of Vascular Surgery, Hospital of the University of Pennsylvania, Philadelphia, PA, USA.
Vasc Endovascular Surg. 2010 Feb;44(2):146-9. doi: 10.1177/1538574409357247.
Behçet's disease is a chronic, relapsing multisystemic inflammatory disorder characterized by recurrent orogenital aphthous ulcers, uveitis, and skin lesions. Vascular involvement occurs in up to 38% of these patients. Herein, we report a 19-year-old male who initially presented with an isolated celiac artery aneurysm that was treated with open surgical repair. The patient was subsequently diagnosed with Behçet's disease after the development of oral aphthous ulcers and multiple recurrent postoperative deep venous thromboses and thoracoabdominal arterial aneurysms. Ultimately, a hybrid approach was undertaken. This is the fifth celiac artery aneurysm ever reported in this patient group and the first to present with an isolated celiac artery aneurysm as the initial manifestation of Behçet's disease.
白塞病是一种慢性复发性多系统炎症性疾病，其特征为复发性口腔生殖器阿弗他溃疡、葡萄膜炎和皮肤病变。这些患者中高达38%会出现血管受累。在此，我们报告一名19岁男性，他最初表现为孤立性腹腔干动脉瘤，接受了开放手术修复治疗。该患者随后在出现口腔阿弗他溃疡、多次复发性术后深静脉血栓形成以及胸腹主动脉瘤后被诊断为白塞病。最终，采取了一种综合治疗方法。这是该患者群体中报道的第五例腹腔干动脉瘤，也是首例以孤立性腹腔干动脉瘤作为白塞病初始表现的病例。
