Service de Radiologie et Imagerie Médicale, Hôtel Dieu, CHU Clermont-Ferrand, Bd Léon Malfreyt, Clermont-Ferrand 63058, France.
Pediatr Radiol. 2010 Jul;40(7):1293-6. doi: 10.1007/s00247-009-1532-y. Epub 2010 Jan 29.
Epithelioid hemangioendothelioma of the liver is a very rare vascular tumour in children with intermediate malignant potential. We present a case in which the typical imaging appearances of coalescent peripheral hepatic masses with capsular retraction contributed to the diagnosis. A positron emission tomography-CT (PET-CT) procedure was performed in staging the disease with a strong suspicion of coeliac nodal involvement confirmed after laparotomy and histological analysis. Our case is unique because of the rarity of the disease, the young age of the child, and proven nodal metastases at initial diagnosis. The use of PET-CT allows better staging at initial diagnosis and thus better management with improved follow-up in these patients.
肝上皮样血管内皮细胞瘤是一种非常罕见的儿童血管肿瘤，具有中等恶性潜能。我们报告了一例病例，其典型的影像学表现为融合性周边肝肿块伴包膜回缩，有助于诊断。在疾病分期时进行了正电子发射断层扫描-计算机断层扫描（PET-CT）检查，强烈怀疑腹腔干淋巴结受累，剖腹探查和组织学分析后得到证实。我们的病例是独特的，因为这种疾病非常罕见，患儿年龄很小，而且在初始诊断时就已经证实存在淋巴结转移。PET-CT 的使用可以在初始诊断时进行更好的分期，从而改善这些患者的治疗效果并进行更好的随访。
