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高安氏病与继发性眼部缺血综合征。

Takayasu's disease and secondary ocular ischemic syndrome.

作者信息

Demir M Necati, Hazirolan Dicle, Altiparmak Ugur E, Acar Mehmet A, Unlü Nurten, Ornek Firdevs

机构信息

1st Ophthalmology, Clinic, Ankara Training and Research Hospital, Ankara, Turkey.

出版信息

J Pediatr Ophthalmol Strabismus. 2010 Jan-Feb;47(1):54-7. doi: 10.3928/01913913-20100106-13. Epub 2010 Jan 21.

Abstract

Takayasu's, or "pulseless," disease is a rare, idiopathic, chronic granulomatous vasculitis that affects large arterial blood vessels. Ocular manifestations occur as a consequence of obliteration of the carotid artery, and ocular ischemia may develop. A 14-year-old girl with progressive visual loss and ocular ischemic syndrome secondary to Takayasu's disease is described.

摘要

高安氏病,即“无脉症”,是一种罕见的、特发性的、慢性肉芽肿性血管炎,会影响大动脉血管。眼部表现是由于颈动脉闭塞所致,可能会发展为眼部缺血。本文描述了一名14岁患有高安氏病继发进行性视力丧失和眼部缺血综合征的女孩。

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