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以双侧眼部缺血综合征为表现的高安动脉炎

Takayasu Arteritis Presenting as Bilateral Ocular Ischemic Syndrome.

作者信息

Larrazabal Ramon B, Chiu Harold Henrison C, Magbitang-Santiago Angeline Therese

机构信息

Department of Medicine, Philippine General Hospital, University of the Philippines Manila, Manila, Philippines.

Division of Endocrinology, Diabetes, and Metabolism, Department of Medicine, Philippine General Hospital, University of the Philippines Manila, Manila, Philippines.

出版信息

Vasc Specialist Int. 2020 Sep 30;36(3):163-169. doi: 10.5758/vsi.200031.

DOI:10.5758/vsi.200031
PMID:32868487
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7531293/
Abstract

A 26-year-old female came in with progressive blurring of vision. She had developed memory loss and complained of headache, significant weight loss, and exertional left calf pain after prolonged walking. Pertinent physical findings included light perception on visual acuity examination, and the brachial and radial pulses of both arms were not appreciable. Thoracic and abdominal aortic imaging by computed tomography with contrast revealed narrowing along the thoracic aorta and its branches. Carotid Doppler showed bilaterally thickened walls in the common carotid arteries, with near total occlusion of the left carotid artery. These findings were consistent with bilateral ocular ischemic syndrome in Takayasu arteritis. She was given methylprednisolone 500 mg intravenously daily for 3 days with noted improvement in vision. She was discharged and showed improvement on prednisone 35 mg/day and aspirin 80 mg/day. On follow-up two weeks post-discharge, she reported being able to see silhouettes of persons and objects.

摘要

一名26岁女性因视力逐渐模糊前来就诊。她出现了记忆力减退,并伴有头痛、体重显著减轻以及长时间行走后左小腿用力时疼痛。相关体格检查发现包括视力检查仅存光感,双臂肱动脉和桡动脉搏动未触及。胸部和腹部主动脉增强CT成像显示胸主动脉及其分支变窄。颈动脉多普勒检查显示双侧颈总动脉壁增厚,左侧颈动脉几乎完全闭塞。这些发现符合高安动脉炎所致的双侧眼部缺血综合征。给予她静脉注射甲泼尼龙500毫克,每日1次,共3天,视力有明显改善。她出院后服用泼尼松35毫克/天和阿司匹林80毫克/天,病情有所好转。出院两周后随访时,她报告能够看到人和物体的轮廓

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8295/7531293/8e7bd1e61c3d/VSI-36-163-f4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8295/7531293/aa26e4186428/VSI-36-163-f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8295/7531293/cf5d68cf8d21/VSI-36-163-f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8295/7531293/e7cebf238292/VSI-36-163-f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8295/7531293/8e7bd1e61c3d/VSI-36-163-f4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8295/7531293/aa26e4186428/VSI-36-163-f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8295/7531293/cf5d68cf8d21/VSI-36-163-f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8295/7531293/e7cebf238292/VSI-36-163-f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8295/7531293/8e7bd1e61c3d/VSI-36-163-f4.jpg

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本文引用的文献

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Abnormal Retinal Vasculature in a Young Child: A Diagnostic Dilemma.幼儿的视网膜血管异常:诊断难题。
Ocul Immunol Inflamm. 2021 Jan 2;29(1):175-178. doi: 10.1080/09273948.2019.1672199. Epub 2019 Oct 31.
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Bilateral ocular ischemic syndrome as a manifestation of Takayasu arteritis in children.双侧眼部缺血综合征作为儿童高安动脉炎的一种表现形式。
Can J Ophthalmol. 2019 Jun;54(3):e105-e108. doi: 10.1016/j.jcjo.2018.08.018. Epub 2018 Nov 23.
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Epidemiology of Takayasu arteritis.大动脉炎的流行病学
前葡萄膜炎、巩膜炎的模仿者及误诊——角膜专科医生的小贴士与技巧
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Ocular Manifestations of Takayasu's Arteritis-A Case-Based Systematic Review and Meta-Analysis.高安动脉炎的眼部表现——基于病例的系统评价与荟萃分析
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Therapeutic Management of Ocular Ischemia in Takayasu's Arteritis: A Case-Based Systematic Review.Takayasu 动脉炎致眼部缺血的治疗管理:基于病例的系统评价。
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'Eye is a window to the pulse': bilateral ocular ischaemic syndrome as a presenting manifestation of Takayasu arteritis.“眼睛是脉搏的窗口”:双侧眼部缺血综合征作为大动脉炎的首发表现
BMJ Case Rep. 2013 Apr 29;2013:bcr2013009461. doi: 10.1136/bcr-2013-009461.
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