Department of Neurology, St. Adalbert Hospital, Gdańsk, Poland.
Neurol Sci. 2010 Apr;31(2):219-22. doi: 10.1007/s10072-010-0219-3. Epub 2010 Feb 5.
Axial myoclonus (AM) is characterized by sudden muscle jerks involving axial and proximal muscles. It includes propriospinal myoclonus (PSM) which consists of trunk flexion or extension jerking with activity arising in axial muscles and spreading to caudal and rostral muscles at low velocity along propriospinal pathways. We report on two patients displaying flexion AM jerks in the absence of structural lesion of the central nervous system or electrophysiological evidence of organic origin. A conversion disorder was diagnosed. The jerks disappeared after psychoeducation with the patients remaining symptom free in 6-year long follow-up. The diagnoses of psychogenic axial (propriospinal-like) myoclonus were established. The literature on psychogenic axial (propriospinal-like myoclonus) is limited to a case report. Our cases demonstrate a good response to psychotropic medication and psychoeducation and fulfill the psychogenic movement disorder criteria. The phenomenology of psychogenic abnormal movements is diverse and PSM-like clinical picture may be a novel presentation.
轴向肌阵挛(AM)的特征是突然的肌肉抽搐,涉及轴向和近端肌肉。它包括固有脊髓肌阵挛(PSM),其由躯干弯曲或伸展抽搐组成,活动源自轴向肌肉,并以低速度沿着固有脊髓途径向尾部和头部肌肉扩散。我们报告了两名患者,他们在中枢神经系统结构损伤或电生理有机起源证据缺失的情况下出现屈曲性 AM 抽搐。诊断为转换障碍。在对患者进行心理教育后,抽搐消失,6 年的随访中患者无任何症状。诊断为心因性轴向(固有脊髓样)肌阵挛。心因性轴向(固有脊髓样肌阵挛)的文献仅限于病例报告。我们的病例表明对精神药物和心理教育有良好的反应,并符合心因性运动障碍的标准。心因性异常运动的表现多种多样,固有脊髓样临床表现可能是一种新的表现。