Department of Pediatrics, Fernandez Hospital Hyderabad, Hyderabad, India.
Indian J Pediatr. 2010 Mar;77(3):332-4. doi: 10.1007/s12098-010-0022-4. Epub 2010 Feb 8.
Congenital chylothorax is a rare entity which is characterized by abnormal accumulation of chyle in pleural cavity. Chylothorax presenting as non-immune hydrops is even rarer. We report a case of congenital bilateral chylothorax presenting as non immune hydrops and managed successfully with chemical pleurodesis. A term male baby presented at birth with bilateral pleural effusions and subcutaneous edema. It was initially managed with ventilation and intercostals drainage (ICD). After the initiation of feeds, re-accumulation of pleural fluid led to the diagnosis of congenital chylothorax. Management with ICD and octreotide was unsuccessful but responded to chemical pleurodesis with 4% povidine iodine done on 3 separate occasions.
先天性乳糜胸是一种罕见的疾病，其特征是乳糜在胸腔内异常积聚。以非免疫性水肿为表现的乳糜胸则更为罕见。我们报告了一例以非免疫性水肿为表现的先天性双侧乳糜胸病例，并成功地通过化学性胸膜固定术进行了治疗。一名足月男性婴儿出生时即出现双侧胸腔积液和皮下水肿。最初采用通气和肋间引流（ICD）进行治疗。在开始喂养后，胸腔积液再次积聚，导致诊断为先天性乳糜胸。采用 ICD 和奥曲肽进行治疗无效，但通过 3 次 4%聚维酮碘的化学性胸膜固定术治疗后获得了成功。
