Kaderli Aysel Aydin, Baran Ibrahim, Sağ Saim, Biçer Murat, Aker Sibel
Department of Cardiology, Uludag University Faculty of Medicine, Uludag University, Bursa, Turkey.
Heart Surg Forum. 2010 Feb;13(1):E28-30. doi: 10.1532/HSF98.20091123.
Primary sarcoma of the pulmonary artery (PSPA) is an extremely rare tumor of the cardiovascular system. The prognosis is very poor. The clinical symptoms and imaging findings imitate those of pulmonary emboli, causing delays in diagnosis. In this case report, we describe a 73-year-old man with PSPA who initially was admitted with exertional shortness of breath. Transthoracic echocardiographic evaluation revealed 2 masses in the pulmonary artery causing pulmonary hypertension. The patient underwent operation, but he could not be weaned off cardiopulmonary bypass at the end of the operation and died. Pathologic examination of the masses revealed pulmonary sarcoma. Although this patient was admitted to our clinic only 2 weeks after the initial symptoms, he already had distal metastases.
肺动脉原发性肉瘤（PSPA）是一种极其罕见的心血管系统肿瘤。预后非常差。其临床症状和影像学表现与肺栓塞相似，导致诊断延误。在本病例报告中，我们描述了一名73岁患有PSPA的男性，他最初因劳力性气短入院。经胸超声心动图评估发现肺动脉内有2个肿块，导致肺动脉高压。患者接受了手术，但术后无法脱离体外循环，最终死亡。肿块的病理检查显示为肺肉瘤。尽管该患者在出现初始症状仅2周后就住进了我们的诊所，但他已经出现了远处转移。
