Institut Claudius Regaud, Surgery, 20-24, Rue du Pont Saint Pierre, 31052 Toulouse, France.
Surg Oncol. 2012 Mar;21(1):1-5. doi: 10.1016/j.suronc.2009.12.004. Epub 2010 Feb 26.
Pseudomyxoma peritonei (PMP) arising from urachal tumors is extremely rare. To our knowledge, natural history, tumor biological behaviour, morbidity, treatment, and prognosis of PMP arising from the urachus are determined by the associated PMP. Management of urachal tumors with associated PMP should be based on aggressive locorregional therapy with cytoreductive surgery and hyperthermic intraperitoneal chemotherapy, similar to PMP arising from other origins.
脐尿管肿瘤衍生的假性黏液瘤（PMP）极为罕见。据我们所知，脐尿管 PMP 的自然病史、肿瘤生物学行为、发病率、治疗和预后取决于伴发的 PMP。伴发 PMP 的脐尿管肿瘤的治疗应基于积极的局部区域性治疗，包括细胞减灭术和腹腔热灌注化疗，类似于其他来源的 PMP。
