Division of Hematology, Marmara University, Istanbul, Turkey.
Ren Fail. 2010 Jan;32(2):273-6. doi: 10.3109/08860220903573286.
A patient with idiopathic myelofibrosis with nephrotic syndrome is reported. Seven months after the initial diagnosis of myelofibrosis, the patient was presented with dyspnea, generalized edema, heavy proteinuria, massive pleural effusion, and ascites. Renal biopsy showed focal segmental glomerulosclerosis. After starting immunosuppressive therapy consisting of cyclosporine and steroids, his renal function and proteinuria improved and transfusion requirements decreased.
现报道一例特发性骨髓纤维化伴肾病综合征患者。在最初诊断为骨髓纤维化 7 个月后，患者出现呼吸困难、全身水肿、大量蛋白尿、大量胸腔积液和腹水。肾活检显示局灶节段性肾小球硬化。开始使用环孢素和类固醇组成的免疫抑制疗法后，他的肾功能和蛋白尿改善，输血需求减少。
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