Azorín Daniel, Torrelo Antonio, Lassaletta Alvaro, de Prada Inmaculada, Colmenero Isabel, Contra Trinidad, González-Mediero Imelda
Department of Pathology, Hospital del Niño Jesús, 28009 Madrid, Spain.
Pediatr Dermatol. 2009 Nov-Dec;26(6):709-12. doi: 10.1111/j.1525-1470.2009.01018.x.
Juvenile xanthogranuloma is a benign and self-limited disease which usually appears in the skin of children. Visceral involvement has been rarely reported, as has fatal outcome in some affected individuals. We report a case of systemic juvenile xanthogranuloma in a female newborn with mainly skin, bone marrow, and liver involvement, leading to death at the age of 2 months.
幼年性黄色肉芽肿是一种良性自限性疾病,通常出现在儿童皮肤。内脏受累情况鲜有报道,部分受累个体出现致命结局的情况也不多见。我们报告一例女性新生儿全身性幼年性黄色肉芽肿病例,主要累及皮肤、骨髓和肝脏,患儿于2个月龄时死亡。