1 型神经纤维瘤病相关的恶性外周神经鞘瘤伴心脏转移：病例报告。
Malignant peripheral nerve sheath tumor associated with neurofibromatosis type 1, with metastasis to the heart: a case report.
机构信息
Department of Pathology, Osaka Medical Center for Cancer and Cardiovascular Diseases, 1-3-3 Nakamichi, Higashinari, Osaka, Japan.
出版信息
Diagn Pathol. 2010 Jan 9;5:2. doi: 10.1186/1746-1596-5-2.
A rare case is presented of a 61-year-old man with a malignant peripheral nerve sheath tumor associated with neurofibromatosis type 1, with metastasis to the heart. The primary tumor originated in the right thigh in 1982. Since then, the patient has had repeated local recurrences in spite of repeated surgical treatment and adjuvant chemotherapy. He has developed previous metastases of the lung and heart. The patient died of cardiac involvement.
现报告 1 例罕见病例：61 岁男性，患有与神经纤维瘤病 1 型相关的恶性外周神经鞘瘤，伴有心脏转移。1982 年，原发性肿瘤起源于右大腿。此后，尽管反复进行手术治疗和辅助化疗，患者仍反复出现局部复发。他曾发生过肺部和心脏的先前转移。患者因心脏受累而死亡。
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