Institute of Pathology-ICMR, Safdarjung Hospital, New Delhi, India.
Indian J Dermatol Venereol Leprol. 2010 Mar-Apr;76(2):176-9. doi: 10.4103/0378-6323.60573.
Primary adenoid cystic carcinoma (PCACC) of skin is a rare tumor, and those who show distant metastasis are even rarer. We report a case of PCACC on the face of a 55-year-old man who showed bilateral lung metastasis and on palliative chemotherapy showed significant regression of the primary tumor. The patient was alive at a 15-month follow-up. A brief literature review of the eight cases including ours is described.
皮肤原发性腺样囊性癌（PCACC）较为罕见，发生远处转移者更为罕见。我们报告了 1 例发生于 55 岁男性面部的 PCACC 患者，该患者发生了双侧肺转移，接受姑息性化疗后原发肿瘤明显退缩。患者在 15 个月的随访中存活。本文描述了包括我们的病例在内的 8 例患者的简要文献复习。
