Premalatha S, Sarveswari K N, Lahiri Koushik
Department of Dermatology, Stanley Medical College and Hospital, Chennai, India.
Indian J Dermatol. 2010;55(1):86-91. doi: 10.4103/0019-5154.60360.
Ehlers-Danlos Syndrome (EDS) is a rare group of inheritable connective tissue disorder of defective collagen. Skin, joints and blood vessels are most commonly affected. Clinical signs such as Gorlin sign and Metenier sign have been described in this syndrome. We report another new clinical sign called 'Reverse-Namaskar' sign as an important clinical finding in EDS, based on the family pedigree study of the proband.
埃勒斯-当洛综合征（EDS）是一组罕见的遗传性胶原蛋白缺陷性结缔组织疾病。皮肤、关节和血管最常受累。该综合征已描述了诸如戈尔林征和梅滕尼尔征等临床体征。基于先证者的家系研究，我们报告了另一种新的临床体征——“反向合十礼”征，作为埃勒斯-当洛综合征的一项重要临床发现。
