Williams Judson B, McCann Richard L, Hughes G Chad
Division of Thoracic and Cardiovascular Surgery, Department of Surgery, Duke University Medical Center, Durham, North Carolina, USA.
J Card Surg. 2011 May;26(3):304-8. doi: 10.1111/j.1540-8191.2011.01224.x. Epub 2011 Mar 28.
Loeys-Dietz syndrome (LDS) is a recently identified genetic complex characterized in part by rapidly progressive aortic and branch vessel disease. We now describe total aortic replacement using an open Extent II thoracoabdominal repair followed by second-stage redo-sternotomy for a valve-sparing aortic root replacement and hybrid aortic arch repair in a patient with this syndrome.
洛伊氏-迪茨综合征(LDS)是一种最近才被确认的遗传性综合征,部分特征为主动脉和分支血管疾病进展迅速。我们现在描述了在一名患有该综合征的患者中,采用开放性Ⅱ型胸腹联合修复进行全主动脉置换,随后进行二期再次胸骨切开术以保留瓣膜的主动脉根部置换和杂交主动脉弓修复。