奥斯勒-韦伯-伦杜（OWR）病与心力衰竭。
Osler-Weber-Rendu (OWR) Disease and Heart Failure.
作者信息
Blum Arnon, Shalabi Rafea
机构信息
Department of Medicine, Baruch-Padeh Poria Medical Center, Lower Galilee Israel.
出版信息
Clin Med Cardiol. 2009 Nov 25;3:121-3. doi: 10.4137/cmc.s3636.
Abstract
OWR is a genetic disease, transmitted as an autosomal dominant disorder characterized by arteriovenous malformations predominantly involving the mucocutaneous epithelium. One of the significant complications is the development of arteriovenous fistulas in different organs like the liver and brain. One of the rarest complications of this arteriovenous conduit is a high-output heart failure. We would like to describe a 66 years old woman who was admitted with a high-output cardiac failure who deteriorated clinically and was treated successfully by conservative management.
摘要
OWR是一种遗传性疾病，以常染色体显性疾病形式传播，其特征是动静脉畸形主要累及黏膜皮肤上皮。其中一个重要并发症是在肝脏和大脑等不同器官形成动静脉瘘。这种动静脉通道最罕见的并发症之一是高输出量心力衰竭。我们想描述一位66岁因高输出量心力衰竭入院的女性患者，其临床症状恶化，经保守治疗成功治愈。
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