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儿童特发性嗜酸性粒细胞增多综合征伴发脑炎。

Encephalitis in idiopathic hypereosinophilic syndrome in childhood.

机构信息

Department of Pediatrics, Medical Research Institute, Pusan National University College of Medicine, 1-10, Ami-Dong, Seo-Ku, Pusan, 602-739, Korea.

出版信息

Pediatr Radiol. 2010 Dec;40 Suppl 1:S130-3. doi: 10.1007/s00247-010-1718-3. Epub 2010 Jun 4.

DOI:10.1007/s00247-010-1718-3
PMID:20523982
Abstract

Idiopathic hypereosinophilic syndrome (IHES) is a heterogeneous spectrum of disorders characterized by hypereosinophilia and the presence of dysfunction in various end organs without an identifiable underlying cause. Neurological manifestations, including peripheral neuropathy, encephalopathy and cerebral thromboembolic or hemorrhagic disorders, can exist with IHES. We present a unique case of a 14-year-old girl with IHES and encephalitis involving the right temporo-parieto-occipital cortex.

摘要

特发性嗜酸性粒细胞增多综合征(IHES)是一组异质性疾病,其特征为嗜酸性粒细胞增多和各种终末器官功能障碍,但无明确的潜在病因。IHES 可伴有神经系统表现,包括周围神经病、脑病和脑血栓栓塞或出血性疾病。我们报告了一例 14 岁女孩 IHES 合并累及右颞顶枕叶皮质的脑炎的独特病例。

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1
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