Department of Neurology, Amedeo Avogadro University, corso Mazzini 18, Novara, Italy.
Neurol Sci. 2010 Dec;31(6):821-4. doi: 10.1007/s10072-010-0331-4. Epub 2010 Jun 5.
The association of Moyamoya disease (MD) with other cerebrovascular disease has been reported in literature but not the occurrence of MD and arteriovenous fistula of the epiaortic vessels. A 61-year old Italian woman was admitted to our Department because of the sudden onset of Broca's aphasia. At general examination she presented a murmur above the right clavicle. Brain magnetic resonance imaging (MRI) showed an ischemic lesion involving left frontal and temporal lobes. Cerebral digital subtraction angiography (DSA) showed moyamoya vessels and an arteriovenous fistula between vertebral artery and internal giugular vein in right laterocervical region. This is the first report of the association of MD with arteriovenous fistula of the epiaortic vessels.
文献中报道了烟雾病（MD）与其他脑血管病的关联，但并未报道过 MD 与主动脉外血管动静脉瘘的同时发生。一位 61 岁的意大利女性因突发布罗卡失语症而入住我院。一般检查时，她在右锁骨上方可闻及杂音。脑部磁共振成像（MRI）显示左额颞叶存在一处缺血性病变。脑数字减影血管造影（DSA）显示右侧颈侧区椎动脉和颈内静脉之间存在烟雾病血管和动静脉瘘。这是 MD 与主动脉外血管动静脉瘘关联的首例报告。
