Department of Dermatology, Chang Gung Memorial Hospital, Taipei, Taiwan.
Australas J Dermatol. 2010 Aug;51(3):198-201. doi: 10.1111/j.1440-0960.2010.00630.x.
Ulceration of non-caseating granulomas is a rare cutaneous presentation of sarcoidosis. Granulomatous vasculitis is classically associated with Wegener's granulomatosis, lymphomatoid granulomatosis or Churg-Strauss syndrome. It is also commonly noted in pulmonary sarcoidosis, but has seldom been reported in cutaneous sarcoidosis, particularly the ulcerative variant. We present a rare case of sarcoidosis with multiple purpuric leg ulcers showing a granulomatous vasculitis histologically.
非干酪样肉芽肿的溃疡是结节病的一种罕见皮肤表现。肉芽肿性血管炎通常与韦格纳肉芽肿、淋巴瘤样肉芽肿病或变应性肉芽肿性血管炎有关。它也常见于肺结节病,但在皮肤结节病中很少见,特别是溃疡性变异型。我们报告一例罕见的结节病病例,其多发性紫癜性腿部溃疡表现为组织学上的肉芽肿性血管炎。