难治性先天性乳糜性腹水

Refractory congenital chylous ascites.

作者信息

Melo-Filho Antônio Aldo, Souza Ivana Jesus Nogueira, Leite Christiane Araújo Chaves, Leite Robério Dias, Colares João Henrique Freitas, Correia Júlio Marcus Sousa

机构信息

Department of Surgery, Medical School, Federal University of Ceará (UFC), Rua Professor Costa Mendes, 1608, 3° andar, Rodolfo Teófilo, CEP: 60430-140, Fortaleza, Ceará, Brazil.

出版信息

Indian J Pediatr. 2010 Nov;77(11):1335-7. doi: 10.1007/s12098-010-0193-z. Epub 2010 Sep 7.

DOI:10.1007/s12098-010-0193-z

PMID:20821276

Abstract

Refractory congenital chylous ascites (CCA) is an uncommon clinical condition. Few cases have been described and no gold standard treatment has been defined so far. This report describes a case of refractory CCA in a newborn child which was treated by surgery. Preoperative lower-limb lymphoscintigraphy associated with intraoperative patent blue testing and fibrin glue application were useful in order to provide a successful outcome.

摘要

难治性先天性乳糜腹水（CCA）是一种罕见的临床病症。目前仅有少数病例被报道，且尚未确定金标准治疗方法。本报告描述了一例通过手术治疗的新生儿难治性CCA病例。术前下肢淋巴闪烁显像术联合术中专利蓝试验及纤维蛋白胶应用有助于取得成功的治疗效果。