Paediatric Liver, GI & Nutrition Centre, King's College Hospital, London, UK.
Eur J Pediatr. 2011 May;170(5):573-81. doi: 10.1007/s00431-010-1309-1. Epub 2010 Oct 2.
Acute liver failure in neonates is rare, but carries a high mortality. Neonatal liver failure can be defined as "failure of the synthetic function of liver within 4 weeks of birth". Encephalopathy is not essential for the diagnosis. Acute liver failure in neonates differs from children with regard to aetiology and outcome. Common causes of neonatal liver failure are neonatal hemochromatosis, haematological malignancies, viral infections and liver-based metabolic defects. Early diagnosis and referral to a paediatric liver centre is recommended as liver transplantation is the only definitive treatment when supportive or a disease-specific treatment fails.
新生儿急性肝衰竭较为罕见,但死亡率较高。新生儿肝衰竭可定义为“出生后 4 周内肝脏合成功能衰竭”。肝性脑病并非诊断所必需。新生儿肝衰竭的病因和预后与儿童有所不同。新生儿肝衰竭的常见病因包括新生儿血色素沉着症、血液系统恶性肿瘤、病毒感染和肝脏代谢缺陷。建议早期诊断并转至儿科肝脏中心,因为当支持治疗或针对特定疾病的治疗无效时,肝移植是唯一的确定性治疗方法。