Department of Pediatrics, First Affiliated Hospital, Sun Yat-sen University, 58 Zhongshan Road II, Guangzhou, 510080, People's Republic of China.
Indian J Pediatr. 2011 Mar;78(3):345-7. doi: 10.1007/s12098-010-0256-1. Epub 2010 Oct 16.
Congenital chylous ascites (CCA) is a rare disease defined as the accumulation of chylomicron-rich lymphatic fluid within the peritoneal cavity, resulting from maldevelopment of the intra-abdominal lymphatic system. Cases unresponsive to conservative treatment usually require surgical intervention. We report a case of CCA in a premature neonate, who was treated successfully with intravenous infusion of octreotide, a synthetic somatostatin analogue after failure to response to traditional supportive therapies.
先天性乳糜性腹水(CCA)是一种罕见疾病,定义为腹腔内乳糜微粒丰富的淋巴液积聚,是由于腹腔内淋巴系统发育不良所致。对保守治疗无反应的病例通常需要手术干预。我们报告了一例早产儿 CCA 病例,在传统支持治疗无效后,经静脉输注合成生长抑素类似物奥曲肽成功治疗。