Paul G K, Sen B, Bari M A, Hossain M A, Bari M S, Chanda S K, Siddique S R, Azam M G, Khan T A
Department of Cardiology, Mymensingh Medical College (MMC), Mymensingh, Bangladesh.
Mymensingh Med J. 2010 Oct;19(4):614-7.
Primary Cardiac tumors are uncommon during infancy and childhood. Myxomas originating in the right ventricles are even less common in paediatric patient. Our patient baby Rani, 3 months of age presented with shortness of breath and chest indrawing. Antenatal history and delivery was uneventful. The baby was under weight and also malnourished but there was no cyanosis and clubbing. Her respiratory rate was 25/minute. On precordium examination, first heart sound (S1) was normal but pulmonary component of second heart sound (P2) was soft. There was an ejection systolic murmur (Grade-3/6) in the left upper para-sternal area. Chest X-ray revealed cardiomegaly. Echocardiogram revealed a large mass (11x10mm) in the right ventricle, dynamically obstructing the right ventricular out-flow tract and compressing the left ventricle. There was a Tricuspid regurgitation (Grade-2) and moderate pulmonary hypertension (PASP-50 mmHg).
原发性心脏肿瘤在婴儿期和儿童期并不常见。起源于右心室的黏液瘤在儿科患者中更为罕见。我们的患者拉尼宝宝,3个月大,出现呼吸急促和胸廓凹陷。产前病史和分娩过程均正常。婴儿体重不足且营养不良,但无发绀和杵状指。她的呼吸频率为每分钟25次。在心前区检查时,第一心音(S1)正常,但第二心音的肺动脉成分(P2)较弱。在胸骨左缘上部区域有一个喷射性收缩期杂音(3/6级)。胸部X线显示心脏扩大。超声心动图显示右心室内有一个大肿块(11×10mm),动态阻塞右心室流出道并压迫左心室。存在三尖瓣反流(2级)和中度肺动脉高压(肺动脉收缩压-50mmHg)。