Department of Clinical Sciences, University "Sapienza", Policlinico Umberto I, 00165 Rome, Italy.
Endocrine. 2010 Dec;38(3):313-9. doi: 10.1007/s12020-010-9394-5.
Primary aldosteronism (PA) with synchronous carcinoid syndrome is extremely rare occurrence. In this article, we describe a case of PA due to adrenocortical adenoma ("aldosteronoma") and concurrent malignant carcinoid tumor of ileum. The patient was treated with synchronous right adrenalectomy and resection of the ileum. This case is an example of concomitant presence of two types of tumors, effectively managed surgically. We report a case of a nonclassical form of multiple endocrine neoplasia type 1 (MEN 1) syndrome.
原发性醛固酮增多症(PA)伴同步类癌综合征极为罕见。本文描述了一例由肾上腺皮质腺瘤(“醛固酮瘤”)和回肠恶性类癌肿瘤引起的 PA 病例。患者接受了同步右侧肾上腺切除术和回肠切除术。该病例是两种类型肿瘤同时存在的一个例子,通过手术有效治疗。我们报告了一例非典型 1 型多发性内分泌肿瘤(MEN 1)综合征。