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成人眼眶横纹肌肉瘤

Orbital rhabdomyosarcoma in an adult.

作者信息

Lavaju P, Das H, Malla P, Tiwari A, Sinha A, Upadhyaya P

机构信息

Department of Ophthalmology, B.P. Koirala Institute of Health Sciences, Dharan, Nepal.

出版信息

Nepal J Ophthalmol. 2010 Jan-Jun;2(1):64-7. doi: 10.3126/nepjoph.v2i1.3707.

Abstract

INTRODUCTION

Rhabdomyosarcoma is the most common primary orbital malignant tumor in children. Orbital lesions represent about 10 % of all the cases of rhabdomyosarcoma. Rhabdomyosarcoma is a rare cause of proptosis in adults.

OBJECTIVE

To report a case of primary orbital rhabdomyosarcoma in a 45-year-old female.

DESIGN

Interventional case report. The main outcome measures are a rare cause ofproptosis in an adult, discussion on treatment options and prognosis ofrhabdomyosarcoma.

RESULT

The patient underwent total orbital exenteration and was referred for radiotherapy and chemotherapy.

CONCLUSION

Rhabdomyosarcoma is a rare cause of proptosis in adults. It should be suspected in a case of rapidly-progressive proptosis in adults.

摘要

引言

横纹肌肉瘤是儿童最常见的原发性眼眶恶性肿瘤。眼眶病变约占所有横纹肌肉瘤病例的10%。横纹肌肉瘤是成人眼球突出的罕见原因。

目的

报告一例45岁女性原发性眼眶横纹肌肉瘤病例。

设计

介入性病例报告。主要观察指标为成人眼球突出的罕见原因、横纹肌肉瘤治疗方案及预后的讨论。

结果

患者接受了全眶内容剜除术,并接受放疗和化疗。

结论

横纹肌肉瘤是成人眼球突出的罕见原因。成人出现快速进展性眼球突出时应怀疑此病。

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