Torrisi J M, Haller J O, Velcek F T
Department of Radiology, SUNY Health Science Center, Brooklyn 11203.
AJR Am J Roentgenol. 1990 Dec;155(6):1273-6. doi: 10.2214/ajr.155.6.2122679.
The radiologic findings in five neonates with choledochal cyst associated with extra-hepatic biliary atresia are described. All five patients (age range, 13-72 days) presented with jaundice and acholic stools. In all four patients who underwent sonographic examination, a cystic structure separate from the gallbladder representing the choledochal cyst was shown. The diagnosis of atresia of the distal common bile duct was made preoperatively in all cases by hepatobiliary scintigraphy. Diagnosis was confirmed by surgical findings and was demonstrated by intraoperative cholangiography in four cases. All patients were successfully treated with surgical intervention within 1 month from the time of diagnosis. Early detection of this rare disorder, which may be distinct from choledochal cyst found in children and adults, is important to prevent fatal complications of biliary obstruction. The combined use of sonography and hepatobiliary scintigraphy can correctly identify this subset of patients with persistent neonatal jaundice and provide valuable information for prompt surgical management.
本文描述了5例患有胆总管囊肿合并肝外胆管闭锁的新生儿的影像学表现。所有5例患者（年龄范围为13 - 72天）均表现为黄疸和陶土样便。在接受超声检查的4例患者中，均显示出一个与胆囊分离的囊性结构，即胆总管囊肿。所有病例术前均通过肝胆闪烁显像诊断为胆总管远端闭锁。诊断经手术结果证实，4例经术中胆管造影证实。所有患者在诊断后1个月内均成功接受了手术干预。早期发现这种可能与儿童及成人胆总管囊肿不同的罕见疾病，对于预防胆道梗阻的致命并发症很重要。超声检查和肝胆闪烁显像的联合应用能够正确识别这一持续性新生儿黄疸患者亚组，并为及时的手术治疗提供有价值的信息。
