Hsu C C, Lin L H, Chen D F
Department of Pediatrics and Surgery, Cathay General Hospital, Taipei, Taiwan, R.O.C.
Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi. 1997 Jul-Aug;38(4):300-2.
Choledochal cysts are malformations of the biliary ductal system, which rarely occur in infancy. In neonates and infants, choledochal cysts are congenital, may be associated with distal biliary atresia and typically presents with cholestatic jaundice and acholic stools characteristic of biliary obstruction. In older children and adults, it may be acquired in association with an anomalous pancreaticobiliary union and presents with any combination of intermittent jaundice, abdominal pain, and a palpable abdominal mass. Early detection of choledochal cysts is important in the prevention of the fatal complications of biliary obstruction. Here, we present two cases of congenital choledochal cyst in which the patients were 9 weeks old and 7 weeks old respectively. Both of them presented with jaundice, acholic stools, and hepatomegaly. Combined use of sonography, computed tomography and hepatobiliary scintigraphy demonstrated the presence of choledochal cysts. Thereafter, they underwent surgical excision of the cysts with Roux-en-Y reconstruction of the biliary tree; the results were successful.
胆总管囊肿是胆管系统的畸形,在婴儿期很少发生。在新生儿和婴儿中,胆总管囊肿是先天性的,可能与远端胆管闭锁有关,通常表现为胆汁淤积性黄疸和胆汁性梗阻特有的无胆汁粪便。在大龄儿童和成人中,它可能是后天获得性的,与胰胆管异常合流有关,表现为间歇性黄疸、腹痛和可触及的腹部肿块的任何组合。早期发现胆总管囊肿对于预防胆管梗阻的致命并发症很重要。在此,我们报告两例先天性胆总管囊肿病例,患者分别为9周龄和7周龄。他们均表现为黄疸、无胆汁粪便和肝肿大。超声、计算机断层扫描和肝胆闪烁显像的联合应用证实了胆总管囊肿的存在。此后,他们接受了囊肿的手术切除并进行了胆管树的Roux-en-Y重建;结果成功。