Schwill Simon, Kallenbach Klaus, Beller Carsten J, Karck Matthias
Department of Cardiac Surgery, University Hospital Heidelberg, INF 110, D-69120 Heidelberg, Germany.
Interact Cardiovasc Thorac Surg. 2011 Apr;12(4):526-8. doi: 10.1510/icvts.2010.256123. Epub 2011 Jan 12.
Acute aortic dissection type-A (AADA) is a life-threatening condition especially in patients with Marfan syndrome (MFS) simultaneously suffering from severe pectus excavatum (PE). We report on emergency surgery for combined treatment of PE and AADA in a patient with MFS using an alternative approach. It leads to excellent exposure of the dislocated heart and great vessels enabling Bentall procedure followed by funnel chest repair with modified technique of Adkins and Blades. We achieved favorable functional and cosmetic results. Therefore, we conclude the surgical approach presented is feasible for standard treatment of AADA and consecutive repair of PE.
急性A型主动脉夹层（AADA）是一种危及生命的疾病，尤其是在患有马凡综合征（MFS）且同时患有严重漏斗胸（PE）的患者中。我们报告了一例采用替代方法对患有MFS的患者进行PE和AADA联合治疗的急诊手术。该方法能很好地暴露脱位的心脏和大血管，从而可行Bentall手术，随后采用改良的阿德金斯和布莱兹技术修复漏斗胸。我们取得了良好的功能和美容效果。因此，我们得出结论，所提出的手术方法对于AADA的标准治疗和随后的PE修复是可行的。
