眼眶上皮样肉瘤
Epithelioid sarcoma of the orbit.
作者信息
Alkatan Hind M, Chaudhry Imtiaz, Al-Qahtani Abdullah
机构信息
Department of Pathology and Laboratory Medicine, Oculoplastic and Orbital Division, King Khaled Eye Specialist Hospital, Riyadh, Saudi Arabia.
出版信息
Ann Saudi Med. 2011 Mar-Apr;31(2):187-9. doi: 10.4103/0256-4947.75589.
Epithelioid sarcoma is an aggressive and rare malignancy first recognized by Enzinger in 1970. It is known most commonly to affect the distal upper extremities in young adults. The classical "distal" form has a male predominance and can also involve other less frequent sites including lower extremities, proximal upper extremities, and the trunk. The "proximal" variant of this tumor is deep seated, tends to occur in older patients and predominantly develops in the pelvis, perineum, and genital tract. In the orbit, only a single report of two cases, which had a typical histopathologic appearance, has been previously published. We present the third case of orbital primary epithelioid sarcoma.
上皮样肉瘤是一种侵袭性罕见恶性肿瘤，1970年由恩津格首次发现。它最常见于影响年轻成年人的上肢远端。典型的“远端”型以男性居多，也可累及其他较少见的部位，包括下肢、上肢近端和躯干。这种肿瘤的“近端”变体位置较深，往往发生在老年患者中，主要发生在骨盆、会阴和生殖道。在眼眶，此前仅发表过一篇关于两例具有典型组织病理学表现病例的报告。我们报告第三例眼眶原发性上皮样肉瘤。
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