University of Kent, UK.
Am J Intellect Dev Disabil. 2011 Jan;116(1):65-80. doi: 10.1352/1944-7558-116.1.65.
Fragile X syndrome is the most common inherited cause of intellectual and developmental disability. The influence of environmental variables on behaviors associated with the syndrome has received only scant attention. The current study explored the function served by problem behavior in fragile X syndrome by using experimental functional analysis methodology with 8 children with fragile X. No child met criteria for attention-maintained problem behavior, 5 children met criteria for escape-maintained problem behavior, and 4 children met criteria for tangible-maintained problem behavior. Results are discussed and compared with previous findings on the function of problem behavior in fragile X syndrome, and implications for intervention are discussed. It is noted that the external validity of these findings is limited by the small sample size.
脆性 X 综合征是最常见的遗传性智力和发育障碍的原因。环境变量对与该综合征相关的行为的影响仅受到很少的关注。本研究使用实验功能分析方法对 8 名脆性 X 综合征儿童进行了研究,探讨了问题行为在脆性 X 综合征中的作用。没有儿童符合注意力维持问题行为的标准,5 名儿童符合逃避维持问题行为的标准,4 名儿童符合有形维持问题行为的标准。结果与脆性 X 综合征中问题行为功能的先前发现进行了讨论和比较,并讨论了干预的意义。需要注意的是,这些发现的外部有效性受到样本量小的限制。