Department of Neurology, Philipps University Marburg, Marburg, Germany.
Neurodegener Dis. 2011;8(6):438-46. doi: 10.1159/000325829. Epub 2011 May 12.
Multiple system atrophy (MSA) and progressive supranuclear palsy (PSP), known as atypical parkinsonian syndromes (APS), are neurodegenerative disorders with severe disability and decreased life expectancy. Little is known about the health-related quality of life (HrQoL) and its determinants in patients with those disorders. The objective of our cross-sectional study was to evaluate the HrQoL in patients with APS and to identify the determinants of HrQoL.
A total of 101 consecutive patients with MSA (n = 54) and PSP (n = 47) were recruited in four German neurological centers. Disease severity was assessed using the Hoehn and Yahr stages and the Unified MSA Rating Scale. The HrQoL was evaluated using the EuroQol instrument (EQ-5D and EQ-VAS). Independent determinants of HrQoL were identified in multiple regression analyses.
The mean EQ-VAS score was 52% lower than that reported for the general population (36.9 ± 18.3 vs. 77.4 ± 19.0). Of the study participants, 63% reported severe problems in at least one dimension of the EQ-5D. Cerebellar dysfunction was associated with a more considerable reduction of HrQoL. Independent determinants of reduced HrQoL were female gender, <12 years of education, disease severity, a decreased number of persons in the household and depression.
The HrQoL in MSA and PSP is considerably reduced. While therapeutic options in the treatment of motor symptoms remain restricted, greater attention should be paid to the treatment of depression, which was identified among independent determinants of HrQoL. Independent determinants of HrQoL should be considered when developing healthcare programs aimed at improving the HrQoL in APS.
多系统萎缩(MSA)和进行性核上性麻痹(PSP),称为非典型帕金森综合征(APS),是具有严重残疾和降低预期寿命的神经退行性疾病。关于这些疾病患者的健康相关生活质量(HrQoL)及其决定因素知之甚少。我们的横断面研究目的是评估 APS 患者的 HrQoL,并确定 HrQoL 的决定因素。
我们从四个德国神经科中心招募了 101 例连续 MSA(n = 54)和 PSP(n = 47)患者。使用 Hoehn 和 Yahr 分期和统一 MSA 评分量表评估疾病严重程度。使用 EuroQol 工具(EQ-5D 和 EQ-VAS)评估 HrQoL。使用多元回归分析确定 HrQoL 的独立决定因素。
平均 EQ-VAS 评分比一般人群报告的低 63%(36.9 ± 18.3 比 77.4 ± 19.0)。研究参与者中有 63%的人报告在 EQ-5D 的至少一个维度存在严重问题。小脑功能障碍与 HrQoL 的显著降低相关。HrQoL 降低的独立决定因素是女性、<12 年教育程度、疾病严重程度、家庭人数减少和抑郁。
MSA 和 PSP 的 HrQoL 明显降低。虽然治疗运动症状的选择仍然有限,但应更加关注抑郁的治疗,抑郁是 HrQoL 的独立决定因素之一。在制定旨在改善 APS 患者 HrQoL 的医疗保健计划时,应考虑 HrQoL 的独立决定因素。