Department of Radiology, First Affiliated Hospital of ZhengZhou University, Zhengzhou, Henan, China.
J Korean Med Sci. 2011 Jun;26(6):832-5. doi: 10.3346/jkms.2011.26.6.832. Epub 2011 May 18.
Pancreatoblastoma is a rare primary pancreatic neoplasm of children that may arise in any portion of the pancreas. We report a case of a 3-yr-old boy who presented to with abdominal pain our hospital and a progressive bulge in his right abdomen. Biochemical evaluation and serum levels of tumoral markers were within reference limits. On the computed tomography, two tumors were found. One located in the head of the pancreas; however, a laparotomy revealed that the head of pancreas was compressed but normal. The other was in the left abdomen near the spleen and the tail of the pancreas. The diagnosis of two synchronous pancreatoblastoma originating from the omentum was confirmed by pathology. Therefore, a pancreatoblastoma should be considered when a large well-defined, lobulated, and heterogeneous mass is identified in the pancreas of children. In addition, an ectopic pancreatoblastoma should be considered when identified within or near the ectopic pancreatic tissue.
胰腺母细胞瘤是一种罕见的儿童胰腺原发性肿瘤,可发生于胰腺的任何部位。我们报告了一例 3 岁男孩,因腹痛和右腹部逐渐膨隆就诊于我院。生化评估和肿瘤标志物血清水平均在参考范围内。在计算机断层扫描中发现了两个肿瘤。一个位于胰头部;然而,剖腹探查显示胰头部受压但正常。另一个位于脾脏和胰尾部附近的左侧腹部。病理证实两个同步起源于大网膜的胰腺母细胞瘤的诊断。因此,当在儿童胰腺中发现大而界限清楚、分叶状和异质性的肿块时,应考虑胰腺母细胞瘤。此外,当在异位胰腺组织内或附近发现胰腺母细胞瘤时,也应考虑异位胰腺母细胞瘤。