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播散性腹膜平滑肌瘤病患者的随访:一例罕见高危病例报告

Follow-up in patients with disseminated peritoneal leiomyomatosis: a report of an unusual, high-risk case.

作者信息

Jeyarajah Santhini, Chow Andre, Lloyd Josephine, Zacharakis Emmanouil, Purkayastha Sanjay, Tekkis Paris

机构信息

St Mary's Hospital, Academic Surgical Unit, Praed Street, London, W2 1NY, UK.

出版信息

BMJ Case Rep. 2009;2009. doi: 10.1136/bcr.08.2008.0802. Epub 2009 Mar 20.

Abstract

Leiomyomatosis peritonei disseminata is a condition seen uncommonly in states of oestrogen hypersecretion in women of childbearing age. There are no clear guidelines for the primary management and follow-up of these patients. Here, a rare case in a postmenopausal woman with a normal hormonal state who may be considered higher risk is presented, with a review suggesting a management pathway in these patients.

摘要

播散性腹膜平滑肌瘤病是一种在育龄期女性雌激素分泌过多状态下罕见的病症。对于这些患者的初始管理和随访尚无明确指南。在此,本文呈现了一例处于正常激素状态的绝经后女性的罕见病例,该病例可能被认为风险较高,并通过文献综述提出了这类患者的管理途径。

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本文引用的文献

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Leiomyomatosis peritonealis disseminata with malignant transformation.播散性腹膜平滑肌瘤病伴恶性转化
Int J Gynaecol Obstet. 1999 Jul;66(1):43-5. doi: 10.1016/s0020-7292(98)00255-0.

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