Dubrey Simon William, Hillson Rowan, Dahdal Maher
Hillingdon Hospital, Cardiology, Pield Heath Road, Uxbridge UB8 3NN, UK.
BMJ Case Rep. 2009;2009. doi: 10.1136/bcr.07.2008.0546. Epub 2009 Mar 17.
ARTERIOVENOUS MALFORMATION (AVM) OCCURRING IN ASSOCIATION WITH SOFT TISSUE AND SKELETAL HYPERTROPHY FORMS THE BASIS OF THE PARKES WEBER SYNDROME: a rare congenital angio-osteohypertrophy condition with no obvious racial, gender or geographic preference. Usually in the lower limbs, the AVM can result in a dilated cardiomyopathy due to a high output cardiac state. We describe the case of a 21-year-old woman with an extensive AVM affecting one leg, which included the pelvic vasculature. The case concerns assessment of the current high output "heart failure" and her cardiovascular risk from future pregnancy.
与软组织和骨骼肥大相关的动静脉畸形（AVM）构成了帕克斯·韦伯综合征的基础：这是一种罕见的先天性血管骨肥大病症，无明显种族、性别或地域倾向。AVM通常发生于下肢，由于高心输出量状态可导致扩张型心肌病。我们描述了一名21岁女性的病例，其一条腿（包括盆腔血管）患有广泛的AVM。该病例涉及对当前高输出量“心力衰竭”的评估以及她未来妊娠的心血管风险。
