Islam Farrah, Azad Nadia, Khan Ayesha
Department of Ophthalmology, Al-Shifa Trust Eye Hospital, Rawalpindi.
J Coll Physicians Surg Pak. 2011 Jun;21(6):374-5.
Iridocorneal endothelial syndrome is described to be a rare, usually unilateral ocular condition in young females. There are three known overlapping clinical variants of this condition namely, essential iris atrophy, Cogan-Reese and Chandler syndrome. We report a case of bilateral iridocorneal endothelial (ICE) syndrome with microspherophakia. A 25 years old female presented with microspherophakic lens dislocated into anterior chamber in right eye, and displaced inferiorly in left eye. She was also diagnosed with ICE syndrome and underwent lensectomies in both eyes. This unique combination has never been reported before.
虹膜角膜内皮综合征被描述为一种罕见的、通常发生在年轻女性的单侧眼部疾病。这种疾病有三种已知的重叠临床变体，即原发性虹膜萎缩、科根-里斯综合征和钱德勒综合征。我们报告一例双侧虹膜角膜内皮（ICE）综合征合并小晶状体的病例。一名25岁女性，右眼小晶状体脱位至前房，左眼小晶状体向下移位。她还被诊断为ICE综合征，并接受了双眼晶状体切除术。这种独特的组合此前从未有过报道。
