Division of Cardiology, Department of Pediatrics, The Labatt Family Heart Center, The Hospital for Sick Children, University of Toronto School of Medicine, Toronto, Canada.
Catheter Cardiovasc Interv. 2012 Aug 1;80(2):E5-8. doi: 10.1002/ccd.23197. Epub 2011 Dec 8.
Long segment narrowing of the thoracoabdominal aorta or so-called middle aortic syndrome (MAS), is an uncommon lesion presenting variably with physical signs of coarctation of the aorta, hypertension, renal insufficiency and or mesenteric ischemia. The etiologies are multiple, but Takayasu's arteritis is a leading cause. Variable involvement of diverse systemic arterial systems requires individualized management strategies. We report a case of a successful treatment algorithm for severe MAS using a strategy of percutaneous aortic endovascular stent implantation to rebuild the distal aorta and renal auto-implantation to address systemic hypertension.
胸主动脉和腹主动脉的长段狭窄,或所谓的中主动脉综合征(MAS),是一种不常见的病变,其临床表现各不相同,包括主动脉缩窄、高血压、肾功能不全和/或肠系膜缺血的物理征象。病因多种多样,但大动脉炎是主要病因。不同系统动脉的不同程度受累需要个体化的治疗策略。我们报告了一例使用经皮主动脉腔内支架植入术重建远端主动脉和肾自体移植治疗系统性高血压的策略成功治疗严重 MAS 的病例。